Esferocitosis hereditaria. Carolina Cózar Trastorno hemolítico familiar caracterizado por: anemia ictericia intermitente esplenomegalia. Esferocitosis Hereditaria Anemia Esferocitosis Hereditaria 1) Defecto de la membrana del eritrocito. 2) Retención selectiva por el bazo normal. De esta forma es posible el rastreo de la esferocitosis hereditaria y de la Las manifestaciones clínicas como ictericia, esplenomegalia, anemia, aplasia y y sobrecarga de hierro sugiere daño pancréatico por la acumulación, tal como se.

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Long-term evaluation of the beneficial effect of subtotal splenectomy for management of hereditary spherocytosis.

A study of 62 Spanish cases. De esta forma es posible el rastreo de la esferocitosis hereditaria y de la esferocitosis secundaria.

Se recomienda el monitoreo de glucemia y ferritina. HS esrerocitosis a hemolytic defect, frequently increased iron overload was not unexpected. Am J Hematol ;57 1: Monitoring of blood glucose and ferritin is recommended. Servicio de ayuda de la revista.

Esferocitosis hereditaria by Jazmin Cózar Madero on Prezi

Clinico-hematological profile of hereditary spherocytosis: Bienvenido a siicsalud Contacto Inquietudes. Applying criteria such as permanence of an increased percentage of spherocytes, family history, biochemical symptoms of hemolysis and clinical data, we claim a prevalence of generally asymptomatic hereditary spherocytosis HS of 1: Clinical symptoms such as esferociosis, splenomegaly, anemia, aplasia and biliary calculi prompting a diagnosis of HS are in reality rare.

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This explains the discrepancy between these values.

The identity of hyperchromic RBC and spherocytes as well as their normal percentage have been previously established.

Thus it becomes possible to screen for both hereditary and secondary spherocytosis. Patient and physician should be informed of the presence of HS to avoid misinterpretation of concurrent pathological symptoms.

Postoperative pulmonary embolism in a young female accompanying with Factor V Leiden mutation and hereditary sypherocytosis. Oxygen affinity and compensated hemolysis in hereditary spherocytosis. Referencias -Mayelin Herrera Garcia.

Blood Cells Mol Dis ; Abstract Hematological automates using double beam laser diffraction by artificially spherized red blood cells determine both volume and hemoglobin concentration of esfericitosis very large number of cells, even indicating percentages of aberrant elements.

Laparoscopic partial vs total splenectomy in children with hereditary spherocytosis. Erythroid membrane protein defects in hereditary spherocytosis. Hereditary Spherocytosis in Neonates with Hyperbilirubinemia. Splenectomy for hereditary spherocytosis: J Lab Clin Med. Xnemia J Haematol ;93 2: Int J Pediatr Hematol Oncol ; 2: Polish Academjy of Sciences? Aires, Argentina; 16 2: Guidelines for the diagnosis and management of hereditary spherocytosis update.


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Este hecho explica la discrepancia entre estos valores. Journal of Medical Cases. The high association of HS with both diabetes and iron overload suggest damage of the endocrine pancreas by the latter, as it is also seen in genetic hemochromatosis. Hereditary spherocytosis, thrombocytosis, and chronic pulmonary emboli: King on behalf of the General Haematology Task Force of the British Committee for Standards in Haematology Guidelines for the diagnosis and management of hereditary spherocytosis.

J Thromb Thrombolysis ;17 3: Thrombo-embolic disease after splenectomy for hereditary stomatocytosis. Revista Cubana Hematol Inmunol Hemoter ;18 1: The Italian survey on esferocitoxis spherocytosis.